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Artigos da EINA - Deficiências

Distúrbios de Desenvolvimento Embriológico

Anomalias do Septum Pellucidum

O Septum Pellucidum é uma estrutura medial que forma as paredes mediais dos ventrículos laterais localizada logo abaixo do joelho do corpo caloso, entre os cornos anteriores dos ventriculos laterais. Durante o período embrionário é formado por duas lâminas, que se fundem posteriormente. Dois tipos principais de anomalias podem ser observadas: ausência ou persistência do cavum do septum, isto é, a persistência das lâminas embrionárias.

A persistência do cavum do septum foi considerada uma variação normal, mas devido suas associações com vários distúrbios de desenvolvimento embrionário, é considerada agora um indicativo de um desenvolvimento cerebral anômalo. A ausência do septo pode decorrer de um desenvolvimento embrionário falho ou de lesões que afetam o desenvolvimento durante o primeiro trimestre da gravidez.

 


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